Chapter 2 - Higher congitive function

Questions

Define the following terms:

agnosia, agnosagnosia, apraxia, receptive aphasia, expressive aphasia, global aphasia, alexia, agraphia, dysinhibition, dysnomia, paraphasic, paratonia, perseveration.
Agnosia is the inability to recognize what something is despite being able to perceive it. This can be visual, auditory or tactile.
Agnosagnosia is the inability to recognize a particular deficit (for example that one is paralyzed).
Apraxia is the inability to synthesize a complex motor pattern despite having the strength and coordination to perform it.
Receptive aphasia is the inability to understand language (written or verbal).
Expressive aphasia is the inability to synthesize language (written or verbal).
Global aphasia is the inability to either understand or to synthesize language (written or verbal).
Alexia is the inability to read.
Agraphia is the inability to write.
Dysinhibition is the appearance of responses that are normally suppressed. In the context of higher cognitive functions, it is the return of more primitive reflexes or behavior patterns that are normally suppressed by "higher areas" of the brain (often the frontal lobe).
Dysnomia is the inability to name objects.
Paraphasic errors include substituting words that have inappropriate meaning, although the words sound somewhat similar or start with the same sounds. This often happens with receptive aphasias.
Paratonia is an involuntary, irregular resistance to passive movement (it feels like the patient is assisting in movement when they are not attempting to).
Perseveration is repeating motions (or responses) when it is inappropriate to do so.

2-1. Name some cerebral cortical functions that are well localized and unilateral.

Answer 2-1. Well localized, unilateral cortical functions include: somatic sensation, voluntary motor function (especially of hands), expressive language, receptive language, attention to the contralateral world (neglect), understanding of what is wrong (agnosagnosia), vision.

2-2. Name some cerebral cortical functions that are well localized and represented bilaterally.

Answer 2-2. Well-localized and bilateral cortical functions: hearing, short term memory, frontal lobe functions (mood, behavior, emotional control, motivation, executive functions), visuospatial function (parietal lobe)

2-3. Name some cerebral cortical functions that are diffusely represented in the cerebral cortex.

Answer 2-3. Diffuse cerebral cortical functions: long term memory, self and species preservation functions (including many behavioral functions.

2-4. Damage to which cerebral cortex produces aphasia?

Answer 2-4. Aphasia is lateralized to the dominant hemisphere

2-5. What can you say about the ability to write in patients with aphasia?

Answer 2-5. Patients with aphasia will write and read the same way that they speak and comprehend speech, respectively.

2-6. What can you say about the ability of a patient with expressive, receptive, or global aphasia to repeat complex phrases?

Answer 2-6. Patients with expressive, receptive or global aphasia will be unable to repeat complex phrases.

2-7. What can you say about the ability of a patient with transcortical aphasia to repeat complex phrases?

Answer 2-7. Patients with transcortical aphasia will be able to repeat although they may not be able to name objects that are presented to them or to understand language.

2-8. What problems will a patient with a transcortical aphasia have?

Answer 2-8. Transcortical aphasia: will be able to repeat complex phrases but will either be unable to understand complex statements or commands (transcortical receptive) or be unable to come up with names for objects (transcortical motor).

2-9. What are the characteristics of the patient with an expressive aphasia (Broca's)?

Answer 2-9. Epressive aphasia: Broca's area, nonfluent, frustrated, dysnomic, can read and understand speech, telegraphic speech.

2-10. What are the characteristics of the patient with a receptive aphasia (Wernicke's)?

Answer 2-10. Receptive aphasia: Wernicke's area, fluent, not frustrated, dysnomic, can't read or understand complex speech.

2-11. What is the most common lesion to produce alexia without agraphia (can write but can't read)?

Answer 2-11. Damage to the dominant occipital lobe and splenium of corpus callosum can produce alexia without agraphia (can write but can't read).

2-12. What area is involved in immediate recall (for example of a phone number)?

Answer 2-12. Immediate recall is a frontal lobe effect (give back a phone number).

2-13. What area is involved in short-term memory?

Answer 2-13. Short-term memory is a hippocampal function (minutes to hours).

2-14. Where is long-term memory stored?

Answer 2-14. Long-term memory is stored diffusely (only lost if large and diffuse areas are damaged).

2-15. What are "executive functions" and where are they primarily located?

Answer 2-15. Executive functions in dorsolateral prefronal part of frontal lobes - these include sequencing, planning, immediate recall, abstractions.

2-16. Where are the areas involved in most of emotional control and "personality"?

Answer 2-16. The orbital and medial frontal (and anterior cingulate) cortex are involved in emotional control.

2-17. Damage to which hemisphere is more likely to produce depression? Which will more likely produce mania?

Answer 2-17. Left frontal damage often produces depression; right frontal may lead to mania.

2-18. Neglect of one side of the world is most commonly due to damage to what area?

Answer 2-18. The parietal lobe is responsible for attention to contralateral world (damage produces neglect) and knowledge of deficits.

2-19. Agnosagnosia most often results from damage to what area?

Answer 2-19. Agnosagnosia, a lack of recognition of problems, is due to damage to the parietal lobe (especially the non-dominant side).

2-20. What "primitive responses" would be expected to be uncovered by damage to the frontal lobes?

Answer 2-20. disinhibited glabellar, snout, suck, palmomental and grasp reflexes.

2-21. Paratonia is a sign of what?

Answer 2-21. Paratonia results from diffuse cortical dysfunction (some degree may be normal).

2-22. What would you expect to see in the patient with a split corpus callosum?

Answer 2-22. Corpus callosum lesions may prevent information from transferring from one hemisphere to the other. The "left hand does not know what right hand is doing."

2-23. The neocortex provides inhibitory modulation of what four basic drives?

Answer 2-23. Feeding, fighting, fleeing and procreation (the four F's).

2-24. What is the clinical term used to describe diffuse hemispheric disease (one word)?

Answer 2-24. Dementia.

2-25. What are the clinical signs of advanced dementia?

Answer 2-25. Loss of cognitive, intellectual functions in more than one sphere of function.

2-26. What regressive reflexes emerge with loss of cortical inhibition?

Answer 2-26. Dysinhibition of glabellar response, palmomental reflex, grasp reflex, suck reflex, rooting reflex, snout reflex and loss of nuchocephalic reflex.

2-27. What are the functions of the limbic areas of the brain?

Answer 2-27. Self and species preservation functions, the "four F's" and emotional reactivity.

2-28. Of 100 people, how many will have significant R hemispheric representation of speech functions? Of these, how many will have bilateral speech representation?

Answer 2-28. 1% right dominant and 2% mixed.

2-29. What percentage of R-handed people are L-hemisphere dominant for speech?

Answer 2-29. About 99.9%.

2-30. What percentage of L-handed people are L-hemisphere dominant for speech?

Answer 2-30. About 70%.

2-31. Below what age can speech function be recovered if the dominant hemisphere is damaged?

Answer 2-31. Age four.

2-32. What are dysfunctions of speech called? What is a complete loss of speech called?

Answer 2-32. Dysphonia (if hoarseness due to mechanical problems in larynx), dysarthria (if due to problems with cranial nerves or cerebellum) or aphasia (this is actually a language problem, not just speech problem). Dysphasia is incomplete, aphasia complete loss of language function.

2-33. A patient with verbal language dysfunction, homonymous hemianopsia, right visual field deficit and little motor deficit most likely has what type of dysphasia?

Answer 2-33. Receptive (Wernicke's) - this is because Wernicke's area is closer to the parietal lobe (and the optic radiations).

2-34. A patient with verbal language dysfunction, marked hemimotor and hemisensory deficit, and no visual abnormality most likely has what type of dysphasia?

Answer 2-34. Expressive (Broca's) - this is because Broca's area is closer to the motor cortex.

2-35. Where is Broca's area located? Where is Wernicke's area located? Name the fasciculus that links the two of them.

Answer 2-35. Broca's - Inferior frontal lobe, just anterior to motor cortex and near Sylvian fissure; Wernicke's - posterior part of superior temporal gyrus; the arcuate (superior longitudinal) fasciculus connects these language areas.

2-36. What gyrus is important in language, especially in word retrieval?

Answer 2-36. Angular gyrus.

2-37. Do most patients with dysphasia have Broca's, Wernicke's, or a combination of both? Why is this so?

Answer 2-37. Combination because they are in same vascular distribution on same side.

2-38. What language abnormalities are manifested with a lesion to Broca's area? Wernicke's area? Angular gyrus? Arcuate (superior longitudinal) fasciculus?

Answer 2-38. Broca's - expressive aphasia; Wernicke's - conductive aphasia; Angular - dysnomic aphasia; Arcuate fasciculus - conductive aphasia.

2-39. What part of the corpus callosum transfers COMPLEX [i.e., verbal] visual info between the two hemispheres?

Answer 2-39. The splenium.

2-40. What are the predominant functions of the R cerebral hemisphere?

Answer 2-40. Visuospatial functions, attention to contralateral world, musicality.

2-41. Which patient will be more motivated to recover from a hemispheric lesion, one with damage on the L or the R?

Answer 2-41. The left (the right hemisphere lesion can result in a lack of appreciation for deficits and therefore problems in compensating).

2-42. Where is the location of a lesion that causes visuospatial disorientation? How does this manifest itself?

Answer 2-42. Right parietal lobe. Patients may get lost and have trouble assembling things or figuring out how to make them work.

2-43. What type of lesion will result in the loss of the ability to imprint new information?

Answer 2-43. Hippocampal lesions - medial temporal lobe (bilaterally).

2-44. Can well-learned material be easily destroyed by a focal lesion? Why or why not?

Answer 2-44. No, there is diffuse representation.

2-45. What three categories of questions need to be asked when testing a patient for problems with learning and memory?

Answer 2-45. Immediate recall; short term recall (several minutes after distraction); recall of remote events.

2-46. What evidence would lead to the conclusions that a demented patient has disease localized primarily in the frontal lobes (i.e., what are the manifestations of lesions to the frontal lobes)?

Answer 2-46. Emotional lability, personality change and/or loss of executive functions.

2-47. What is the effect of lesions localized to the medial aspect of the frontal lobes (parasagittal frontal cortex - supplementary motor area)?

Answer 2-47. Inability to initiate movements (abulia).